Vipin ram ekhar et al 152 rosai-dorfman disease: a rare cause of cervical lymphadenopathy 1vipin ram ekhar, 2ritesh n shelkar, 3sachin rane, 4adharsh anand, 5kanchan lanjewar, 6suresh kumar tarachand jain.  kumar b, karki s, paudyal p diagnosis of sinushistiocytosis with massive lymphadenopathy (rosai-dorfman disease) by fine needle aspiration cytology diagn. Rosai-dorfman disease is a benign lymphohistiocytosis that often involves lymph nodes and presents as massive lymphadenopathy with sinus histocytiosis characterized by painless cervical lymphadenopathy, fever, leukocytosis, elevated esr and polyclonal hypergammaglobulinemia. Rosai-dorfman disease , also known as sinus histiocytosis with massive lymphadenopathy , is a rare disorder of unknown etiology that is characterized by abundant histiocytes in the lymph nodes throughout the body. Rosai-dorfman disease (rdd) is an idiopathic histiocytic proliferative disorder characterized by sinus histiocytosis with massive lymphadenopathy typical clinical presentation involves massive painless cervical lymphadenopathy, but extranodal disease is apparent in about 40 % of cases, most commonly involving the orbit, skin, respiratory.
Rosai-dorfman disease is a rare disorder characterized by accumulation of histiocytes and massive lymphadenopathy, particularly in the neck and head rosai-dorfman disease is most common among patients 20 yr, particularly blacks cause is unknown the most common presenting symptoms are fever and. Rosai dorfman disease (rdd) or sinus histiocytosis is a rare, idiopathic, non neoplastic histiocytic proliferation of unknown etiology typically presenting with massive cervical lymphadenopathy with or without systemic involvement. Rosai-dorfman disease (rdd) is a rare benign histiocyte disorder originally described by rosai and dorfman in 1969 as sinus histiocytosis with lymphadenopathy 1,2 it typically presents as massive, painless cervical lymphadenopathy, and it is most often found in adolescents and young adults.
Rosai-dorfman disease (also known as sinus histiocytosis with massive lymphadenopathy) is a rare non-langerhans'-cell histiocytosis of unknown cause that often manifests as massive cervical. Rosai-dorfman disease is a rare, idiopathic, benign proliferative histiocytic disorder originally described in 1969 5 it is most common in children and adolescents and is typically characterized by massive cervical lymphadenopathy, fevers, leukocytosis, and elevated erythrocyte sedimentation rate 2,3 our patient was atypical in that she. This chapter describes the main features of two different diseases, castleman disease (cd) and rosai-dorfman disease (rdd) castleman disease (cd) is a clinical and histopathologically heterogeneous lymphoproliferative disorder that encompasses at least three distinct entities with some common overlapping morphological features: hyaline vascular cd (hvcd), unicentric plasma cell cd and. Lymphadenopathy or adenopathy is disease of the lymph nodes, in which they are abnormal in size, number, or consistency lymphadenopathy of an inflammatory type (the most common type) is lymphadenitis ,  producing swollen or enlarged lymph nodes.
Sinus histiocytosis with massive lymphadenopathy (rosai-dorfman disease): imaging manifestations in the head and neck review rosai-dorfman disease: manifestations outside of the head and neck. Rosai-dorfman disease is a rare benign disease that was first described by rosai and dorfman as sinus histiocytosis with massive lymphadenopathy in the 1960s 1 this disorder is documented in all age groups, but adolescents are noted to be mostaffected 2 the usual presentation of this disorder includes cervical lymphadenopathy, which is. Destombes-rosai-dorfman' s disease (drd) is an inflammatory non-langerhansian histiocytosis with adenomegaly  , described by destombes in 1965 and later, better defined by rosai and dorfman in 1969 . Also called rosai-dorfman disease massive painless bilateral lymph node enlargement in neck, of unknown etiology rare 25% involve extranodal sites (skin, upper respiratory tract, bone) but massive lymphadenopathy is usually also present. Rosai-dorfman disease (rdd) is a rare idiopathic his to proliferative disorder that usually presents with systemic symptoms and cervical lymphadenopathy intracranial involvement is relatively rare and isolated intracranial rdd is very scarce.
Rosai-dorfman disease (rdd) is a rare histiocytic disorder described as a unique entity by rosai and dorfman in 1969 under the name of sinus histiocytosis with massive lymphadenopathy or shml. Rosai-dorfman disease was first described by rosai and dorfman in 1969 it is a benign disease which is characterized by over-production and accumulation of a specific type of white blood cell (histiocyte) in the lymph nodes of the body, most often those of the neck (cervical. Introduction rosai-dorfman disease (rdd) is a rare proliferative histiocytic disorder of unknown etiology rdd typically presents with generalized lymphadenopathy and polymorphic histiocytic infiltration of the lymph node sinuses however, occurrences of extranodal soft tissue rdd may rarely occur when masquerading as a soft tissue sarcoma.
Rosai-dorfman disease (rdd), originally described as sinus histiocytosis with massive lymphadenopathy, is a rare histiocytic proliferative disorder with a distinctive microscopic appearance patients usually present with massive cervical lymphadenopathy. Rosai-dorfman-destombes disease (rdd) is a rare non-langerhans cell histiocytosis (lch) first described in 1965 by a french pathologist, pierre paul louis lucien destombes, who reported 4 children and young adults with lymphadenopathy and sinus histiocytosis upon histologic analysis 1 four years later, juan rosai and ronald dorfman analyzed. Rosai-dorfman disease was first described by rosai and dorfman in 1969 it is a benign disease which is characterized by over-production and accumulation of a specific type of white blood cell in the lymph nodes of the body, most often those of the neck (cervical.